Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la Las manifestaciones clínicas como ictericia, esplenomegalia, anemia, aplasia y y sobrecarga de hierro sugiere daño pancréatico por la acumulación, tal como se.

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Esferocitosis hereditaria by Jazmin Cózar Madero on Prezi

Hereditary Spherocytosis in Neonates with Hyperbilirubinemia. Clinical symptoms such as jaundice, splenomegaly, anemia, aplasia and biliary calculi prompting a diagnosis of HS are in reality rare. Splenectomy for hereditary spherocytosis: Monitoring of blood glucose esferocjtosis ferritin is recommended.

Journal of Medical Cases. Laparoscopic partial vs total splenectomy in children with hereditary spherocytosis. Applying criteria such as permanence of an increased percentage of spherocytes, family history, biochemical symptoms of hemolysis and clinical data, we claim a prevalence of generally asymptomatic hereditary spherocytosis HS of 1: Se recomienda el monitoreo de glucemia y ferritina.


The Italian survey on hereditary spherocytosis.

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Referencias -Mayelin Herrera Garcia. Este hecho explica la discrepancia entre estos valores.

King on behalf of anwmia General Haematology Task Force of the British Committee for Standards in Haematology Guidelines for the diagnosis and management of hereditary spherocytosis. Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis. Clinico-hematological profile of hereditary spherocytosis: Int J Pediatr Hematol Oncol ; esferociotsis Hereditary spherocytosis, thrombocytosis, and chronic pulmonary emboli: Erythroid membrane protein defects in hereditary spherocytosis.

This explains the discrepancy between these values. Patient and physician should be informed of the presence of HS to avoid misinterpretation of concurrent pathological symptoms.

Anemia Esferocitosis Hereditaria by Danna flores cuadros on Prezi

Bienvenido a siicsalud Contacto Inquietudes. Aires, Argentina; 16 anemka Abstract Hematological automates using double beam laser diffraction by artificially spherized red blood cells determine both volume and hemoglobin concentration of a very large number of cells, even indicating percentages of aberrant elements. J Thromb Thrombolysis ;17 3: Guidelines for the diagnosis and management of hereditary spherocytosis update.


Br J Haematol ;93 2: J Lab Clin Med. HS being a hemolytic defect, frequently increased iron overload was not unexpected. Postoperative pulmonary embolism in a young female accompanying with Factor V Leiden mutation and hereditary sypherocytosis.

Am J Hematol ;57 1: Thus it becomes possible to screen for both hereditary and secondary spherocytosis.

Servicio de ayuda de la revista. The high association of HS with both diabetes and iron overload suggest damage of the endocrine pancreas by the pr, as it is also seen in genetic hemochromatosis. Blood Cells Mol Dis ; Revista Cubana Hematol Inmunol Hemoter ;18 1: Oxygen affinity and compensated hemolysis in hereditary spherocytosis.

De esta forma es posible el rastreo de la esferocitosis hereditaria y de la esferocitosis secundaria. Polish Academjy of Sciences?

A study of 62 Spanish cases. Thrombo-embolic disease after splenectomy for hereditary stomatocytosis.